Islet cell tumor syndrome

Hereditary PHEOCHROMOCYTOMA that originates in ISLET CELLS. Affected individuals have systemic symptoms that may include cerebral hemorrhage, episodic hypertension, sweating, TACHYCARDIA; HYPERTENSIVE RETINOPATHY; CAFÉ-AU-LAIT SPOTS; and excess NOREPINEPHRINE in urine. OMIM: 171420

Also Known As:

Bilateral pheochromocytoma and islet cell adenoma of the pancreas; Chromaffinoma; Familial islet cell tumors; Familial pheochromocytoma

Neoplasms: 1361496
- Neoplasms by Site: 4
  - Digestive System Neoplasms: 251
    - Pancreatic Neoplasms: 35273
      - Islet cell tumor syndrome: 50
  - Endocrine Gland Neoplasms: 135
    - Pancreatic Neoplasms: 35273
      - Islet cell tumor syndrome: 50
- Neoplasms by Histologic Type: 2
  - Germ Cell and Embryonal Neoplasms: 4514
    - Neuroectodermal Tumors: 216
      - Neuroendocrine Tumors: 6524
        Paraganglioma: 2649
        Pheochromocytoma: 9731
        Islet cell tumor syndrome: 50
  - Nerve Tissue Neoplasms: 1
    - Neuroectodermal Tumors: 216
      - Neuroendocrine Tumors: 6524
        Paraganglioma: 2649
        Pheochromocytoma: 9731
        Islet cell tumor syndrome: 50
Digestive System Diseases: 1068
- Pancreatic Diseases: 1654
  - Pancreatic Neoplasms: 35273
    - Islet cell tumor syndrome: 50
- Digestive System Neoplasms: 251
  - Pancreatic Neoplasms: 35273
    - Islet cell tumor syndrome: 50
Endocrine System Diseases: 996
- Endocrine Gland Neoplasms: 135
  - Pancreatic Neoplasms: 35273
    - Islet cell tumor syndrome: 50

Michelle S Linggi Selected Research

Michelle S Linggi Research Topics

Disease

Drug/Important Bio-Agent (IBA)